Osteogenesis Imperfecta Surgical Management of the Femur and Knee

  • Paul Esposito
  • Maegen J. WallaceEmail author

Abstract: Surgical Management: Femoral Shaft/Knee

Osteogenesis imperfecta (OI) has a wide range of presentations and oftentimes presents with recurrent femur fractures and/or significant femoral bowing. The concern with femoral bowing is that as children begin to pull to stand, weight bear, cruise, and walk, they are at an increased risk of femur fractures as there are significant tension stresses across the bowed area. Femur fractures, no matter the age or underlying diagnosis, are extremely painful, and in our opinion, avoiding these significantly painful and potentially traumatic experiences is one of the main goals of surgical treatment for patients with OI, as well as decreasing the need for post-fracture immobilization, which causes further osteoporosis, weakness, and stiffness.


Femoral bowing Recurrent fracture FD rodding Percutaneous osteotomy 


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© Springer Nature Switzerland AG 2020

Authors and Affiliations

  1. 1.College of Medicine Pediatric Orthopaedic SurgeonOrthopaedic Surgery University of Nebraska, Children’s Hospital and Medical CenterDodgeUSA

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