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Osteogenesis Imperfecta Surgical Management of the Femur and Knee

  • Paul Esposito
  • Maegen J. WallaceEmail author
Chapter
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Abstract: Surgical Management: Femoral Shaft/Knee

Osteogenesis imperfecta (OI) has a wide range of presentations and oftentimes presents with recurrent femur fractures and/or significant femoral bowing. The concern with femoral bowing is that as children begin to pull to stand, weight bear, cruise, and walk, they are at an increased risk of femur fractures as there are significant tension stresses across the bowed area. Femur fractures, no matter the age or underlying diagnosis, are extremely painful, and in our opinion, avoiding these significantly painful and potentially traumatic experiences is one of the main goals of surgical treatment for patients with OI, as well as decreasing the need for post-fracture immobilization, which causes further osteoporosis, weakness, and stiffness.

Keywords

Femoral bowing Recurrent fracture FD rodding Percutaneous osteotomy 

References

  1. 1.
    Byers PH, Steiner RD. Osteogenesis imperfecta. Annu Rev Med. 1992;43:269–82.CrossRefGoogle Scholar
  2. 2.
    Forin V, et al. Benefits of pamidronate in children with osteogenesis imperfecta: an open prospective study. Joint Bone Spine. 2005;72(4):313–8.CrossRefGoogle Scholar
  3. 3.
    Fassier F. Osteogenesis imperfecta. In: Duparc J, editor. Surgical techniques in orthopaedics and traumatology. Paris: Elsevier; 2003. p. 1–8.Google Scholar
  4. 4.
    Esposito P, Plotkin H. Surgical treatment of osteogenesis imperfecta: current concepts. Curr Opin Pediatr. 2008;20(1):52–7.CrossRefGoogle Scholar
  5. 5.
    Fassier F. Fassier-Duval telescopic system: how I do it? J Pediatr Orthop. 2017;37(Suppl 2):S48–51.CrossRefGoogle Scholar
  6. 6.
    Esposito P, Fassier F. Multiple percutaneous osteotomies and Fassier-Duval nailing of long bones in osteogenesis imperfecta. In: Wiesel SW, editor. Operative techniques in orthopaedic surgery. Philadelphia: Wolters Kluwer; 2016. p. 1617–29.Google Scholar
  7. 7.
    Azzam KA, et al. Mid-term results of femoral and tibial osteotomies and Fassier-Duval nailing in children with osteogenesis imperfecta. J Pediatr Orthop. 2018;38(6):331–6.CrossRefGoogle Scholar
  8. 8.
    Cho TJ, et al. Locking plate placement with unicortical screw fixation adjunctive to intramedullary rodding in long bones of patients with osteogenesis imperfecta. J Bone Joint Surg Am. 2015;97(9):733.CrossRefGoogle Scholar
  9. 9.
    Franzone JM, Kruse RW. Intramedullary nailing with supplemental plate and screw fixation of long bones of patients with osteogenesis imperfecta: operative technique and preliminary results. J Pediatr Orthop B. 2018;27(4):344–9.CrossRefGoogle Scholar
  10. 10.
    Puvanesarajah V, et al. Prognostic factors associated with pain palliation after spine stereotactic body radiation therapy. J Neurosurg Spine. 2015;23(5):620–9.CrossRefGoogle Scholar
  11. 11.
    Rothschild L, et al. Anesthesia in children with osteogenesis imperfecta: retrospective chart review of 83 patients and 205 anesthetics over 7 years. Paediatr Anaesth. 2018;28(11):1050–1058.8.CrossRefGoogle Scholar
  12. 12.
    Ligier JN, Metaizeau JP, et al. Elastic stable intramedullary nailing of femoral shaft fractures in children. JBJS. 1988;70-B(1):74–7.Google Scholar
  13. 13.
    Puvanesarajah, Shapiro, Sponseller. Sandwich allografts for long-bone nonunions in patients with osteogenesis imperfecta. a retrospective study. J Bone Joint Surg Am. 2015;97:318–25.CrossRefGoogle Scholar

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© Springer Nature Switzerland AG 2020

Authors and Affiliations

  1. 1.College of Medicine Pediatric Orthopaedic SurgeonOrthopaedic Surgery University of Nebraska, Children’s Hospital and Medical CenterDodgeUSA

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