Advertisement

Extremity Surgery in Adults with Osteogenesis Imperfecta

  • Tae-Joon ChoEmail author
Chapter
  • 40 Downloads

Abstract

Osteogenesis imperfecta (OI) requires surgical intervention also in adulthood. Although it is less frequent than in childhood, surgery in adult OI patients has its own characteristic considerations. They still have a greater risk of fracture than normal populations and most of the fractures require surgical intervention. Pre-existing deformity of the long bone and subsequent joint derangement also require surgical intervention. Mild residual deformity persistent from childhood or device implanted in childhood may become symptomatic in middle age or older and also require surgical intervention. Intramedullary rod remains as the mainstay of fixation, while plate and screw is indicated only in limited and special circumstances. Tension band fixation is sometimes useful for fixing metaphyseal fracture or deformity correction. Degenerative joint disease may develop in later life from traumatic arthritis or from malalignment of the limb; joint replacement surgery is technically challenging and its longevity is much shorter than in normal populations.

Keywords

Adult Osteogenesis imperfecta Intramedullary rod Locking plate Fracture healing Deformity correction 

References

  1. 1.
    Cho TJ, Lee K, Oh CW, Park MS, Yoo WJ, Choi IH. Locking plate placement with unicortical screw fixation adjunctive to intramedullary rodding in long bones of patients with osteogenesis imperfecta. J Bone Joint Surg Am. 2015;97:733–7.CrossRefGoogle Scholar
  2. 2.
    Puvanesarajah V, Shapiro JR, Sponseller PD. Sandwich allografts for long-bone nonunions in patients with osteogenesis imperfecta: a retrospective study. J Bone Joint Surg Am. 2015;97:318–25.CrossRefGoogle Scholar
  3. 3.
    Roberts TT, Cepela DJ, Uhl RL, Lozman J. Orthopaedic considerations for the adult with osteogenesis imperfecta. J Am Acad Orthop Surg. 2016;24:298–308.CrossRefGoogle Scholar
  4. 4.
    To M, Gupta V, Chow W. Surgical management of long bone pseudarthrosis with severe limb length discrepancy in osteogenesis imperfecta. J Pediatr Orthop B. 2013;22:63–9.CrossRefGoogle Scholar

Copyright information

© Springer Nature Switzerland AG 2020

Authors and Affiliations

  1. 1.Division of Pediatric OrthopaedicsSeoul National University Children’s HospitalSeoulRepublic of Korea
  2. 2.Department of Orthopaedic SurgerySeoul National University College of MedicineSeoulRepublic of Korea

Personalised recommendations